<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>1688-0390</journal-id>
<journal-title><![CDATA[Revista Médica del Uruguay]]></journal-title>
<abbrev-journal-title><![CDATA[Rev. Méd. Urug.]]></abbrev-journal-title>
<issn>1688-0390</issn>
<publisher>
<publisher-name><![CDATA[Sindicato Médico del Uruguay]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S1688-03902019000200163</article-id>
<article-id pub-id-type="doi">10.29193/rmu.35.2.8</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Angioedema hereditario. Acerca de un caso clínico]]></article-title>
<article-title xml:lang="en"><![CDATA[Hereditary angioedema. A clinical case]]></article-title>
<article-title xml:lang="pt"><![CDATA[Angioedema herediário. Informe de um caso clínico]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Sosa]]></surname>
<given-names><![CDATA[Elizabeth]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Lemos]]></surname>
<given-names><![CDATA[Felipe]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Insagaray]]></surname>
<given-names><![CDATA[Juan]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Rodríguez]]></surname>
<given-names><![CDATA[Ismael]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Universidad de la República Cátedra y Departamento de Hemoterapia y Medicina Transfusional Hospital de Clínicas. Facultad de Medicina]]></institution>
<addr-line><![CDATA[Montevideo ]]></addr-line>
<country>Uruguay</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Universidad de la República Cátedra y Departamento de Hemoterapia y Medicina Transfusional Hospital de Clínicas. Facultad de Medicina]]></institution>
<addr-line><![CDATA[Montevideo ]]></addr-line>
<country>Uruguay</country>
</aff>
<aff id="Af3">
<institution><![CDATA[,Universidad de la República Cátedra y Departamento de Hemoterapia y Medicina Transfusional Hospital de Clínicas. Facultad de Medicina]]></institution>
<addr-line><![CDATA[Montevideo ]]></addr-line>
<country>Uruguay</country>
</aff>
<aff id="Af4">
<institution><![CDATA[,Universidad de la República Cátedra y Departamento de Hemoterapia y Medicina Transfusional Hospital de Clínicas. Facultad de Medicina]]></institution>
<addr-line><![CDATA[Montevideo ]]></addr-line>
<country>Uruguay</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>06</month>
<year>2019</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>06</month>
<year>2019</year>
</pub-date>
<volume>35</volume>
<numero>2</numero>
<fpage>163</fpage>
<lpage>175</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.edu.uy/scielo.php?script=sci_arttext&amp;pid=S1688-03902019000200163&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.edu.uy/scielo.php?script=sci_abstract&amp;pid=S1688-03902019000200163&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.edu.uy/scielo.php?script=sci_pdf&amp;pid=S1688-03902019000200163&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen:  Introducción:  los angioedemas son motivo de consulta frecuente en alergología. Una minoría de ellos representa un desafío diagnóstico-terapéutico y concierne a la medicina transfusional.  Objetivo:  reseñar la presentación clínica y el tratamiento de un paciente con angioedema hereditario.  Material y método:  presentación de un caso clínico incluyendo antecedentes personales, familiares, descripción y reto de la enfermedad con aportes de literatura científica actualizada.  Resultados:  abordaje de la patología en términos clínicos, paraclínicos, terapéuticos y preventivos a partir del caso desarrollado.  Conclusiones:  se logró el encare de una entidad infrecuente y poco conocida con perspectivas de mejora diagnóstico-terapéutica a favor de la calidad de vida de estos pacientes.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract:  Introduction:  angioedemas are a frequent cause of consultation in allergology. A small number of cases imply a diagnostic and therapeutic challenge and involve transfusion medicine.  Objective:  to outline the clinical presentation and handling of a patient with hereditary angioedema.  Method:  presentation of the clinical case including personal and family history, as well as a description and account of the condition&#8217;s challenge with the contribution of updated scientific literature.  Results:  ways of approaching the condition in clinical, paraclinical, therapeutic and prophylactic terms, based on the study of a case.  Conclusions:  the study managed to address this rather unusual and not well known condition, with the prospect of diagnostic and therapeutic improvement for the quality of life of these patients.]]></p></abstract>
<abstract abstract-type="short" xml:lang="pt"><p><![CDATA[Resumo:  Introdução:  os angioedemas são uma causa de consulta frequente em alergologia. Uma pequena porcentagem é um desafio diagnóstico-terapêutico e é objeto de estudo da medicina transfusional.  Objetivo: descrever as características clínicas e o manejo de um paciente com angioedema hereditário.  Método:  apresentação de um caso clínico incluindo antecedentes pessoais, familiares, descrição e desafio da doença e revisão da literatura científica.  Resultados:  abordagem da patologia em termos clínicos, de exames complementares, terapêuticos e preventivos a partir do caso estudado.  Conclusões: estudou-se uma entidade rara e pouco conhecida com perspectivas de melhoria diagnóstico-terapêutica com benefícios para a qualidade de vida destes pacientes.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Angioedemas hereditarios]]></kwd>
<kwd lng="es"><![CDATA[Proteína inhibidora del complemento C1]]></kwd>
<kwd lng="es"><![CDATA[Informes de casos]]></kwd>
<kwd lng="es"><![CDATA[Crisis de angioedema]]></kwd>
<kwd lng="en"><![CDATA[Angioedemas, hereditary]]></kwd>
<kwd lng="en"><![CDATA[Complement C1 inhibitor protein]]></kwd>
<kwd lng="en"><![CDATA[Case reports]]></kwd>
<kwd lng="en"><![CDATA[Angioedema crisis]]></kwd>
<kwd lng="pt"><![CDATA[Angioedemas hereditários]]></kwd>
<kwd lng="pt"><![CDATA[Proteína inibidora do complemento C1]]></kwd>
<kwd lng="pt"><![CDATA[Relatos de casos]]></kwd>
<kwd lng="pt"><![CDATA[Crise de angioedema]]></kwd>
</kwd-group>
</article-meta>
</front><back>
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