<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>2393-6797</journal-id>
<journal-title><![CDATA[Revista Uruguaya de Medicina Interna ]]></journal-title>
<abbrev-journal-title><![CDATA[Rev. Urug. Med. Int.]]></abbrev-journal-title>
<issn>2393-6797</issn>
<publisher>
<publisher-name><![CDATA[Sociedad de Medicina Interna del Uruguay]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S2393-67972025000101311</article-id>
<article-id pub-id-type="doi">10.26445/10.01.25</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Estados Protrombóticos asociados al Síndrome de Budd Chiari: a propósito de una serie de casos]]></article-title>
<article-title xml:lang="en"><![CDATA[Prothrombotic states associated with Budd Chiari syndrome: a case series]]></article-title>
<article-title xml:lang="pt"><![CDATA[Estados protrombóticos associados à síndrome de Budd Chiari: uma série de casos]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[de los Campos]]></surname>
<given-names><![CDATA[Manuela]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Elizondo]]></surname>
<given-names><![CDATA[Martín]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Rey]]></surname>
<given-names><![CDATA[Romina]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Valverde]]></surname>
<given-names><![CDATA[Marcelo]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Hospital Central de las Fuerzas Armadas Unidad Bi-Institucional de Trasplante Hepático - UDA CeNaHBP Servicio de Enfermedades Hepáticas. Centro Nacional Hepato-Bilio-Pancreático]]></institution>
<addr-line><![CDATA[Montevideo ]]></addr-line>
<country>Uruguay</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>00</month>
<year>2025</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>00</month>
<year>2025</year>
</pub-date>
<volume>10</volume>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.edu.uy/scielo.php?script=sci_arttext&amp;pid=S2393-67972025000101311&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.edu.uy/scielo.php?script=sci_abstract&amp;pid=S2393-67972025000101311&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.edu.uy/scielo.php?script=sci_pdf&amp;pid=S2393-67972025000101311&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen:  Introducción: El síndrome de Budd-Chiari es una condición rara e infradiagnosticada, caracterizada por la obstrucción del flujo venoso hepático, que genera hipertensión portal y daño hepático progresivo. Identificar los estados protrombóticos como etiologías subyacentes es fundamental para su diagnóstico y manejo. El objetivo fue analizar y describir los estados protrombóticos asociados al SBC en pacientes tratados en el Programa Nacional de Trasplante Hepático de Uruguay.  Metodología: Estudio retrospectivo y descriptivo de siete pacientes adultos diagnosticados con SBC entre enero de 2014 y diciembre de 2019. Se recolectaron datos etiológicos, demográficos, clínicos y de laboratorio. La evaluación diagnóstica incluyó determinación de proteína C y S, Factor V Leiden, mutación de protrombina G20210A, antitrombina III, síndrome antifosfolipídico (SAF), hemoglobinuria paroxística nocturna, mutación MTHFR y mutación JAK2 V617F.  Resultados: La cohorte incluyó 6 mujeres (85%) y 1 hombre, con una mediana de edad de 31 años. Todos los casos presentaron complicaciones relacionadas con hipertensión portal. Se identificaron etiologías protrombóticas en 6 pacientes: SAF (2), neoplasias mieloproliferativas (2), mutación de protrombina G20210A (1) y enfermedad de Behçet (1). Un caso permaneció idiopático. Cuatro pacientes requirieron trasplante hepático, mientras que tres fueron manejados solo con anticoagulación.  Conclusiones: Los estados protrombóticos son una causa subyacente significativa del SBC, frecuentemente representando la manifestación inicial de una condición trombofílica. Un abordaje multidisciplinario es esencial para el diagnóstico y tratamiento efectivos, particularmente en centros de referencia en hepatología y trasplante hepático.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract:  Introduction: Budd-Chiari Syndrome is a rare and underdiagnosed condition characterized by obstruction of hepatic venous outflow, leading to portal hypertension and progressive liver damage. Identifying prothrombotic states as underlying etiologies is crucial for diagnosis and management. The objective was analyze and describe prothrombotic states associated with BCS in patients treated at Uruguay&#8217;s National Liver Transplant Program.  Methodology: A retrospective, descriptive study of seven adult patients diagnosed with BCS between January 2014 and December 2019. Etiological data were collected, including demographic, clinical, and laboratory findings. Diagnostic evaluation included testing for protein C and S deficiencies, Factor V Leiden, prothrombin mutation G20210A, antithrombin III, antiphospholipid syndrome (APS), paroxysmal nocturnal hemoglobinuria, MTHFR mutation, and JAK2 V617F mutation.  Results: The cohort included 6 females (85%) and 1 male, with a median age of 31 years. All cases presented complications of portal hypertension. Prothrombotic etiologies were identified in six patients: APS (2), myeloproliferative neoplasms (2), prothrombin mutation G20210A (1), and Behçet&#8217;s disease (1). One case remained idiopathic. Four patients required liver transplantation, while three were managed with anticoagulation alone.  Conclusion: Prothrombotic states are a significant underlying cause of BCS, often representing the initial manifestation of a thrombophilic condition. A multidisciplinary approach is essential for effective diagnosis and treatment, particularly in reference centers for hepatology and liver transplantation.]]></p></abstract>
<abstract abstract-type="short" xml:lang="pt"><p><![CDATA[Resumo:  Introdução: A síndrome de Budd-Chiari é uma condição rara e subdiagnosticada, caracterizada pela obstrução do fluxo venoso hepático, que leva à hipertensão portal e ao dano hepático progressivo. Identificar os estados protrombóticos como etiologias subjacentes é essencial para o diagnóstico e manejo. Objetivo fue analisar e descrever os estados protrombóticos associados à SBC em pacientes atendidos no Programa Nacional de Transplante Hepático do Uruguai.  Metodologia: Estudo retrospectivo e descritivo de sete pacientes adultos diagnosticados com SBC entre janeiro de 2014 e dezembro de 2019. Foram coletados dados etiológicos, demográficos, clínicos e laboratoriais. A avaliação diagnóstica incluiu a determinação de proteína C e S, fator V Leiden, mutação da protrombina G20210A, antitrombina III, síndrome antifosfolipídica (SAF), hemoglobinúria paroxística noturna, mutação MTHFR e mutação JAK2 V617F.  Resultados: A coorte incluiu 6 mulheres (85%) e 1 homem, com mediana de idade de 31 anos. Todos os casos apresentaram complicações relacionadas à hipertensão portal. Foram identificadas etiologias protrombóticas em 6 pacientes: SAF (2), neoplasias mieloproliferativas (2), mutação da protrombina G20210A (1) e doença de Behçet (1). Um caso permaneceu idiopático. Quatro pacientes necessitaram de transplante hepático, enquanto três foram tratados apenas com anticoagulação.  Conclusão: Os estados protrombóticos são uma causa subjacente significativa da SBC, frequentemente representando a manifestação inicial de uma condição trombofílica. Uma abordagem multidisciplinar é essencial para o diagnóstico e tratamento eficazes, especialmente em centros de referência em hepatologia e transplante hepático.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Síndrome de Budd-Chiari]]></kwd>
<kwd lng="es"><![CDATA[estados protrombóticos]]></kwd>
<kwd lng="es"><![CDATA[neoplasias mieloproliferativas]]></kwd>
<kwd lng="es"><![CDATA[síndrome antifosfolipídico]]></kwd>
<kwd lng="es"><![CDATA[mutación de protrombina G20210A]]></kwd>
<kwd lng="es"><![CDATA[trasplante hepático]]></kwd>
<kwd lng="en"><![CDATA[Budd-Chiari syndrome]]></kwd>
<kwd lng="en"><![CDATA[prothrombotic states]]></kwd>
<kwd lng="en"><![CDATA[myeloproliferative neoplasms]]></kwd>
<kwd lng="en"><![CDATA[antiphospholipid syndrome]]></kwd>
<kwd lng="en"><![CDATA[prothrombin G20210A mutation]]></kwd>
<kwd lng="en"><![CDATA[liver transplantation]]></kwd>
<kwd lng="pt"><![CDATA[Síndrome de Budd-Chiari]]></kwd>
<kwd lng="pt"><![CDATA[estados protrombóticos]]></kwd>
<kwd lng="pt"><![CDATA[neoplasias mieloproliferativas]]></kwd>
<kwd lng="pt"><![CDATA[síndrome antifosfolipídica]]></kwd>
<kwd lng="pt"><![CDATA[mutação da protrombina G20210A]]></kwd>
<kwd lng="pt"><![CDATA[transplante hepático]]></kwd>
</kwd-group>
</article-meta>
</front><back>
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