<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>1688-9339</journal-id>
<journal-title><![CDATA[Odontoestomatología]]></journal-title>
<abbrev-journal-title><![CDATA[Odontoestomatología]]></abbrev-journal-title>
<issn>1688-9339</issn>
<publisher>
<publisher-name><![CDATA[Facultad de Odontología - Universidad de la República]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S1688-93392025000101423</article-id>
<article-id pub-id-type="doi">10.22592/ode2025n45e423</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Manejo de Queratoquistes Odontogénicos Asociados al Síndrome de Gorlin-Goltz. Revisión de la literatura a propósito de un caso]]></article-title>
<article-title xml:lang="pt"><![CDATA[Manejo de Queratocistos Odontogenicos à Síndrome de Gorlin-Goltz. Revisão da Literatura com Base em um Caso Clínico]]></article-title>
<article-title xml:lang="en"><![CDATA[Management of Odontogenic Keratocysts Tumors Associated with Gorlin-Goltz Syndrome. A Literature Review Based on a Case Report]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Avendaño]]></surname>
<given-names><![CDATA[Arturo Javier Henríquez]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
<xref ref-type="aff" rid="Aaf"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Conejeros]]></surname>
<given-names><![CDATA[Sebastian Alberto Galleguillos]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
<xref ref-type="aff" rid="Aaf"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Fernández Ibáñez]]></surname>
<given-names><![CDATA[José Tomás]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
<xref ref-type="aff" rid="Aaf"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Lobos Esparza]]></surname>
<given-names><![CDATA[Mauricio Alejandro]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
<xref ref-type="aff" rid="Aaf"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Mardones Muñoz]]></surname>
<given-names><![CDATA[Marcelo Eduardo]]></given-names>
</name>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Córdova Jara]]></surname>
<given-names><![CDATA[Luis Alberto]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
<xref ref-type="aff" rid="Aaf"/>
<xref ref-type="aff" rid="A a"/>
<xref ref-type="aff" rid="A3"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Hospital San José, Independencia Servicio de Cirugía Maxilofacial ]]></institution>
<addr-line><![CDATA[Santiago ]]></addr-line>
<country>Chile</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Universidad de Chile Facultad de Odontología ]]></institution>
<addr-line><![CDATA[Santiago ]]></addr-line>
<country>Chile</country>
</aff>
<aff id="Af3">
<institution><![CDATA[,Universidad de Chile Facultad de Odontología ]]></institution>
<addr-line><![CDATA[Santiago ]]></addr-line>
<country>Chile</country>
</aff>
<aff id="Af4">
<institution><![CDATA[,Universidad Mayor Facultad de Odontología ]]></institution>
<addr-line><![CDATA[Santiago ]]></addr-line>
<country>Chile</country>
</aff>
<aff id="Af5">
<institution><![CDATA[,Universidad del Desarrollo Facultad de Odontología ]]></institution>
<addr-line><![CDATA[Concepción ]]></addr-line>
<country>Chile</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>00</month>
<year>2025</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>00</month>
<year>2025</year>
</pub-date>
<volume>27</volume>
<numero>45</numero>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.edu.uy/scielo.php?script=sci_arttext&amp;pid=S1688-93392025000101423&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.edu.uy/scielo.php?script=sci_abstract&amp;pid=S1688-93392025000101423&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.edu.uy/scielo.php?script=sci_pdf&amp;pid=S1688-93392025000101423&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen El objetivo de este artículo es describir y discutir, con base en la literatura actual, un caso de un paciente joven con síndrome de Gorlin-Goltz (SGG), destacando el enfoque terapéutico y el desafío que representa la alta tasa de recidiva de los queratoquistes odontogénicos (QO) en SGG. Se presenta un paciente de 19 años con SGG y múltiples QO tratados mediante descompresión, enucleación y tratamiento de la cavidad con solución de Carnoy modificada (SCM). Posteriormente, tres años después acude nuevamente por recidiva de QO, optando en esta nueva instancia por la enucleación y tratamiento de la cavidad con SCM del QO de menor tamaño. Mientras que en el QO de mayor tamaño se realizó la descompresión. Actualmente la conducta clínica frente a los QO no varía entre individuos con y sin SGG, pese a sus diferencias clínicas y moleculares. Por lo tanto, destacamos la necesidad de establecer un tratamiento específico para los QO en pacientes con SGG. El cual podría considerar a los fármacos inhibidores de la vía Sonic Hedgehog (SHH) como tratamiento coadyuvante.]]></p></abstract>
<abstract abstract-type="short" xml:lang="pt"><p><![CDATA[Resumo O objetivo deste artigo é descrever e discutir, com base na literatura atual, um caso de um paciente jovem com síndrome de Gorlin-Goltz (SGG), destacando a abordagem terapêutica e o desafio representado pela alta taxa de recidiva dos queratocistos odontogênicos (QO) na SGG. Apresentamos um paciente de 19 anos com SGG e múltiplos QOs tratados por meio de descompressão, enucleação e tratamento da cavidade com solução de Carnoy modificada (SCM). Três anos depois, o paciente retornou devido à recidiva de QOs, e uma nova abordagem foi adotada: enucleação e tratamento da cavidade com SCM para o QO de menor tamanho, enquanto a descompressão foi realizada para o QO de maior tamanho. Atualmente, a conduta clínica frente aos QOs não varia entre indivíduos com e sem SGG, apesar das diferenças clínicas e moleculares. Assim, destacamos a necessidade de estabelecer um tratamento específico para os QOs em pacientes com SGG, considerando os fármacos inibidores da via Sonic Hedgehog (SHH) como uma terapia adjuvante.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract This article aims to describe and discuss, based on current literature, a case of a young patient with Gorlin-Goltz syndrome (GGS), highlighting the therapeutic approach and the challenge posed by the high recurrence rate of odontogenic keratocysts (OKCs) in GGS. We present a 19-year-old patient with GGS and multiple OKCs treated through decompression, enucleation, and cavity treatment with modified Carnoy&#8217;s solution (MCS). Three years later, the patient returned with recurrent OKCs, and a new approach was taken: enucleation and cavity treatment with MCS for the smaller OKC, while decompression was performed for the larger OKC. Currently, OKC clinical management does not differ between individuals with and without GGS, despite their clinical and molecular differences. Therefore, we highlight the need for a specific treatment for OKCs in GGS patients, which could include Sonic Hedgehog (SHH) pathway inhibitors as adjuvant therapy.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Síndrome de Gorlin-Goltz]]></kwd>
<kwd lng="es"><![CDATA[Síndrome de Nevus Basocelular]]></kwd>
<kwd lng="es"><![CDATA[Queratoquiste Odontogénico]]></kwd>
<kwd lng="es"><![CDATA[Vismodegib]]></kwd>
<kwd lng="es"><![CDATA[Sonidegib]]></kwd>
<kwd lng="pt"><![CDATA[Síndrome de Gorlin-Goltz]]></kwd>
<kwd lng="pt"><![CDATA[Síndrome do Nevo Basocelular]]></kwd>
<kwd lng="pt"><![CDATA[Queratocisto Odontogênico]]></kwd>
<kwd lng="pt"><![CDATA[Vismodegib]]></kwd>
<kwd lng="pt"><![CDATA[Sonidegib]]></kwd>
<kwd lng="en"><![CDATA[Gorlin&#8208;Goltz Syndrome]]></kwd>
<kwd lng="en"><![CDATA[Basal Cell Nevus Syndrome]]></kwd>
<kwd lng="en"><![CDATA[Odontogenic Keratocyst]]></kwd>
<kwd lng="en"><![CDATA[Vismodegib]]></kwd>
<kwd lng="en"><![CDATA[Sonidegib]]></kwd>
</kwd-group>
</article-meta>
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