<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>1688-1281</journal-id>
<journal-title><![CDATA[Revista Cirugía del Uruguay]]></journal-title>
<abbrev-journal-title><![CDATA[Cir. Urug.]]></abbrev-journal-title>
<issn>1688-1281</issn>
<publisher>
<publisher-name><![CDATA[Sociedad de Cirugía del Uruguay]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S1688-12812024000101306</article-id>
<article-id pub-id-type="doi">10.31837/cir.urug/8.1.13</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Leiomiosarcoma retroperitoneal: Informe de un caso]]></article-title>
<article-title xml:lang="en"><![CDATA[Retroperitoneal Leiomyosarcoma: Case report]]></article-title>
<article-title xml:lang="pt"><![CDATA[Leiomiossarcoma retroperitoneal: relato de caso]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[López Camarena]]></surname>
<given-names><![CDATA[Luis Miguel]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Gutiérrez Sánchez]]></surname>
<given-names><![CDATA[Paula Lizeth]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Pérez Mena]]></surname>
<given-names><![CDATA[Francisco Alejandro]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Olvera Olvera]]></surname>
<given-names><![CDATA[Marco Antonio]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Cueva]]></surname>
<given-names><![CDATA[Alejandro Esparza]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Espinosa]]></surname>
<given-names><![CDATA[Francisco Aguilar]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,IMSS Hospital general de zona con medicina familiar No.21 cirugía general]]></institution>
<addr-line><![CDATA[león Guanajuato]]></addr-line>
<country>México</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Universidad de Guadalajara  ]]></institution>
<addr-line><![CDATA[ Jalisco]]></addr-line>
<country>México</country>
</aff>
<aff id="Af3">
<institution><![CDATA[,IMSS Hospital general de zona con medicina familiar No.21, cirugía general]]></institution>
<addr-line><![CDATA[león Guanajuato]]></addr-line>
<country>México</country>
</aff>
<aff id="Af4">
<institution><![CDATA[,IMSS Hospital General de zona No.21, cirugía general]]></institution>
<addr-line><![CDATA[Tepatitlán de Morelos Jalisco]]></addr-line>
<country>México</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>00</month>
<year>2024</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>00</month>
<year>2024</year>
</pub-date>
<volume>8</volume>
<numero>1</numero>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.edu.uy/scielo.php?script=sci_arttext&amp;pid=S1688-12812024000101306&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.edu.uy/scielo.php?script=sci_abstract&amp;pid=S1688-12812024000101306&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.edu.uy/scielo.php?script=sci_pdf&amp;pid=S1688-12812024000101306&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen Presentamos el caso de un paciente masculino de 57 años con un leiomiosarcoma retroperitoneal encontrado de manera incidental. Es una patología poco común, la incidencia anual es 2.7 casos por millón de personas. De igual manera, es una enfermedad de evolución silenciosa, por lo que pasa inadvertida hasta que la masa tumoral alcanza un gran tamaño.Los leiomiosarcomas se evidencian como extensas áreas de heterogeneidad y realce heterogéneo, ocasionado por la presencia de necrosis y focos hemorrágicos. Normalmente no hay presencia de calcificaciones y hay ausencia de tejido adiposo, de esta manera que una gran masa retroperitoneal mayor a 10 cm sin contenido graso y necrosis interna variable debe sugerir la posibilidad de un leiomiosarcoma. La eliminación quirúrgica completa es el tratamiento de elección, ésta se debe realizar con márgenes negativos amplios, factor que repercute en el pronóstico, ya que estos tumores tienden a alcanzar un tamaño muy grande y, a menudo, la extirpación amplia es imposible, lo que afecta la supervivencia del paciente. Este tipo de neoplasias tienen un mal pronóstico, pues se sabe que la supervivencia a los 5 años es de aproximadamente 15%, debido a su alta tendencia a la invasión local, metástasis o diagnóstico tardío.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract We present the case of a 57-year-old male patient with a retroperitoneal leiomyosarcoma found incidentally. It is a rare disease, with an annual incidence of 2.7 cases per million people. Likewise, it is a disease with a silent evolution, so it goes unnoticed until the tumor mass reaches a large size. Leiomyosarcomas appear as extensive areas of heterogeneity and heterogeneous enhancement, caused by the presence of necrosis and hemorrhagic foci. Normally, there is no presence of calcifications and there is an absence of adipose tissue, so a large retroperitoneal mass greater than 10 cm with no fat content and variable internal necrosis should suggest the possibility of a leiomyosarcoma. Complete surgical removal is the treatment of choice, and should be performed with wide negative margins, a factor that affects the prognosis, since these tumors tend to reach a very large size and wide excision is often impossible, which affects the patient's survival. This type of neoplasm has a poor prognosis, since it is known that the 5-year survival rate is approximately 15%, due to its high tendency to local invasion, metastasis or late diagnosis.]]></p></abstract>
<abstract abstract-type="short" xml:lang="pt"><p><![CDATA[Resumo Apresentamos o caso de um paciente do sexo masculino, 57 anos, comleiomiossarcoma retroperitoneal encontrado incidentalmente. É umapatologia rara, a incidência anual é de 2,7 casos por milhão de pessoas. Da mesma forma, é umadoença de evolução silenciosa, por issopassadespercebida até que a massa tumoral atinja umtamanho grande. Os leiomiossarcomasaparecem como extensas áreas de heterogeneidade e realce heterogêneo, causadas pela presença de necrose e focos hemorrágicos. Normalmente nãohápresença de calcificações e háausência de tecido adiposo, portantouma grande massa retroperitoneal maior que 10 cm semconteúdo de gordura e necrose interna variáveldeve indicar a possibilidade de leiomiossarcoma. A remoçãocirúrgica completa é o tratamento de escolha, este deve ser realizado com amplas margens negativas, fator que afeta o prognóstico, poisesses tumores tendem a atingir tamanhomuito grande e, muitasvezes, a remoção ampla é impossível, o que prejudica a sobrevida do paciente. Esse tipo de neoplasia apresentamauprognóstico, pois sabe-se que a sobrevida em 5 anos é de aproximadamente 15%, devido à sua alta tendência à invasão local, metástaseou diagnóstico tardio.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Leiomiosarcoma]]></kwd>
<kwd lng="es"><![CDATA[Neoplasias retroperitoneales]]></kwd>
<kwd lng="es"><![CDATA[Sarcoma]]></kwd>
<kwd lng="es"><![CDATA[Cirugía abdominal]]></kwd>
<kwd lng="es"><![CDATA[Resección.]]></kwd>
<kwd lng="en"><![CDATA[Leiomyosarcoma]]></kwd>
<kwd lng="en"><![CDATA[Retroperitoneal neoplasms]]></kwd>
<kwd lng="en"><![CDATA[Sarcoma]]></kwd>
<kwd lng="en"><![CDATA[Abdominal surgery]]></kwd>
<kwd lng="en"><![CDATA[Resection]]></kwd>
<kwd lng="pt"><![CDATA[Leiomiossarcoma]]></kwd>
<kwd lng="pt"><![CDATA[Neoplasias retroperitoneais]]></kwd>
<kwd lng="pt"><![CDATA[Sarcoma]]></kwd>
<kwd lng="pt"><![CDATA[Cirurgia abdominal]]></kwd>
<kwd lng="pt"><![CDATA[Ressecção]]></kwd>
</kwd-group>
</article-meta>
</front><back>
<ref-list>
<ref id="B1">
<label>1</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[von Mehren]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Kane]]></surname>
<given-names><![CDATA[JM]]></given-names>
</name>
<name>
<surname><![CDATA[Agulnik]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Bui]]></surname>
<given-names><![CDATA[MM]]></given-names>
</name>
<name>
<surname><![CDATA[Carr-Ascher]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
<name>
<surname><![CDATA[Choy]]></surname>
<given-names><![CDATA[E]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Soft Tissue Sarcoma, version 2.2022, NCCN Clinical Practice Guidelines in Oncology]]></article-title>
<source><![CDATA[J Natl Compr Canc Netw]]></source>
<year>2022</year>
<volume>20</volume>
<numero>7</numero>
<issue>7</issue>
<page-range>815-33</page-range></nlm-citation>
</ref>
<ref id="B2">
<label>2</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Messiou]]></surname>
<given-names><![CDATA[C]]></given-names>
</name>
<name>
<surname><![CDATA[Moskovic]]></surname>
<given-names><![CDATA[E]]></given-names>
</name>
<name>
<surname><![CDATA[Vanel]]></surname>
<given-names><![CDATA[D]]></given-names>
</name>
<name>
<surname><![CDATA[Morosi]]></surname>
<given-names><![CDATA[C]]></given-names>
</name>
<name>
<surname><![CDATA[Benchimol]]></surname>
<given-names><![CDATA[R]]></given-names>
</name>
<name>
<surname><![CDATA[Strauss]]></surname>
<given-names><![CDATA[D]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Primary retroperitoneal soft tissue sarcoma: Imaging appearances, pitfalls and diagnostic algorithm.]]></article-title>
<source><![CDATA[Eur J Surg Oncol]]></source>
<year>2017</year>
<volume>43</volume>
<numero>7</numero>
<issue>7</issue>
<page-range>1191-8</page-range></nlm-citation>
</ref>
<ref id="B3">
<label>3</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Al-Dasuqi]]></surname>
<given-names><![CDATA[K]]></given-names>
</name>
<name>
<surname><![CDATA[Irshaid]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
<name>
<surname><![CDATA[Mathur]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Radiologic-pathologic correlation of primary retroperitoneal neoplasms]]></article-title>
<source><![CDATA[Radiographics]]></source>
<year>2020</year>
<volume>40</volume>
<numero>6</numero>
<issue>6</issue>
<page-range>1631-57</page-range></nlm-citation>
</ref>
<ref id="B4">
<label>4</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Turgeon]]></surname>
<given-names><![CDATA[MK]]></given-names>
</name>
<name>
<surname><![CDATA[Cardona]]></surname>
<given-names><![CDATA[K]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Retroperitoneal sarcomas]]></article-title>
<source><![CDATA[Surg Clin North Am]]></source>
<year>2022</year>
<volume>102</volume>
<numero>4</numero>
<issue>4</issue>
<page-range>601-14</page-range></nlm-citation>
</ref>
<ref id="B5">
<label>5</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Rajiah]]></surname>
<given-names><![CDATA[P]]></given-names>
</name>
<name>
<surname><![CDATA[Sinha]]></surname>
<given-names><![CDATA[R]]></given-names>
</name>
<name>
<surname><![CDATA[Cuevas]]></surname>
<given-names><![CDATA[C]]></given-names>
</name>
<name>
<surname><![CDATA[Dubinsky]]></surname>
<given-names><![CDATA[TJ]]></given-names>
</name>
<name>
<surname><![CDATA[Bush Jr]]></surname>
<given-names><![CDATA[WH]]></given-names>
</name>
<name>
<surname><![CDATA[Kolokythas]]></surname>
<given-names><![CDATA[O]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Imaging of uncommon retroperitoneal masses]]></article-title>
<source><![CDATA[Radiographics]]></source>
<year>2011</year>
<volume>31</volume>
<numero>4</numero>
<issue>4</issue>
<page-range>949-76</page-range></nlm-citation>
</ref>
<ref id="B6">
<label>6</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Kilkenny]]></surname>
<given-names><![CDATA[JW]]></given-names>
</name>
<name>
<surname><![CDATA[Bland]]></surname>
<given-names><![CDATA[KI]]></given-names>
</name>
<name>
<surname><![CDATA[Copeland]]></surname>
<given-names><![CDATA[EM]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Retroperitoneal sarcoma: the University of Florida experience]]></article-title>
<source><![CDATA[J Am Coll Surg]]></source>
<year>1996</year>
<volume>182</volume>
<numero>4</numero>
<issue>4</issue>
<page-range>329-39</page-range></nlm-citation>
</ref>
<ref id="B7">
<label>7</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Stoeckle]]></surname>
<given-names><![CDATA[E]]></given-names>
</name>
<name>
<surname><![CDATA[Coindre]]></surname>
<given-names><![CDATA[J-M]]></given-names>
</name>
<name>
<surname><![CDATA[Bonvalot]]></surname>
<given-names><![CDATA[S]]></given-names>
</name>
<name>
<surname><![CDATA[Kantor]]></surname>
<given-names><![CDATA[G]]></given-names>
</name>
<name>
<surname><![CDATA[Terrier]]></surname>
<given-names><![CDATA[P]]></given-names>
</name>
<name>
<surname><![CDATA[Bonichon]]></surname>
<given-names><![CDATA[F]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Prognostic factors in retroperitoneal sarcoma: A multivariate analysis of a series of 165 patients of the French Cancer Center Federation Sarcoma Group]]></article-title>
<source><![CDATA[Cancer]]></source>
<year>2001</year>
<volume>92</volume>
<numero>2</numero>
<issue>2</issue>
<page-range>359-68</page-range></nlm-citation>
</ref>
<ref id="B8">
<label>8</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Storm]]></surname>
<given-names><![CDATA[FK]]></given-names>
</name>
<name>
<surname><![CDATA[Mahvi]]></surname>
<given-names><![CDATA[DM]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Diagnosis and management of retroperitoneal soft-tissue sarcoma]]></article-title>
<source><![CDATA[Ann Surg]]></source>
<year>1991</year>
<volume>214</volume>
<numero>1</numero>
<issue>1</issue>
<page-range>2-10</page-range></nlm-citation>
</ref>
<ref id="B9">
<label>9</label><nlm-citation citation-type="book">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Contrera]]></surname>
<given-names><![CDATA[Carlo M]]></given-names>
</name>
<name>
<surname><![CDATA[Heslin]]></surname>
<given-names><![CDATA[Maty J.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Sarcoma de tejidos blandos]]></article-title>
<source><![CDATA[En Sabiston: Tratado de Cirugía: Fundamentos Biológicos de la Práctica Quirúrgica Moderna]]></source>
<year>2022</year>
<edition>21ª edición</edition>
<page-range>p. 734-53</page-range><publisher-loc><![CDATA[Barcelona, España ]]></publisher-loc>
<publisher-name><![CDATA[Elsevier]]></publisher-name>
</nlm-citation>
</ref>
<ref id="B10">
<label>10</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Swallow]]></surname>
<given-names><![CDATA[CJ]]></given-names>
</name>
<name>
<surname><![CDATA[Strauss]]></surname>
<given-names><![CDATA[DC]]></given-names>
</name>
<name>
<surname><![CDATA[Bonvalot]]></surname>
<given-names><![CDATA[S]]></given-names>
</name>
<name>
<surname><![CDATA[Rutkowski]]></surname>
<given-names><![CDATA[P]]></given-names>
</name>
<name>
<surname><![CDATA[Desai]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Gladdy]]></surname>
<given-names><![CDATA[RA]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Management of primary retroperitoneal sarcoma (RPS) in the adult: An updated consensus approach from the transatlantic Australasian RPS working group]]></article-title>
<source><![CDATA[Ann Surg Oncol]]></source>
<year>2021</year>
<volume>28</volume>
<numero>12</numero>
<issue>12</issue>
<page-range>7873-88</page-range></nlm-citation>
</ref>
<ref id="B11">
<label>11</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Devaud]]></surname>
<given-names><![CDATA[N]]></given-names>
</name>
<name>
<surname><![CDATA[Vornicova]]></surname>
<given-names><![CDATA[O]]></given-names>
</name>
<name>
<surname><![CDATA[Abdul Razak]]></surname>
<given-names><![CDATA[AR]]></given-names>
</name>
<name>
<surname><![CDATA[Khalili]]></surname>
<given-names><![CDATA[K]]></given-names>
</name>
<name>
<surname><![CDATA[Demicco]]></surname>
<given-names><![CDATA[EG]]></given-names>
</name>
<name>
<surname><![CDATA[Mitric]]></surname>
<given-names><![CDATA[C]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Leiomyosarcoma: Current Clinical Management and Future Horizons]]></article-title>
<source><![CDATA[Surg Oncol Clin N Am]]></source>
<year>2022</year>
<volume>31</volume>
<numero>3</numero>
<issue>3</issue>
<page-range>527-46</page-range></nlm-citation>
</ref>
<ref id="B12">
<label>12</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Gilbeau]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
<name>
<surname><![CDATA[Kantor]]></surname>
<given-names><![CDATA[G]]></given-names>
</name>
<name>
<surname><![CDATA[Stoeckle]]></surname>
<given-names><![CDATA[E]]></given-names>
</name>
<name>
<surname><![CDATA[Lagarde]]></surname>
<given-names><![CDATA[P]]></given-names>
</name>
<name>
<surname><![CDATA[Thomas]]></surname>
<given-names><![CDATA[L]]></given-names>
</name>
<name>
<surname><![CDATA[Kind]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Surgical resection and radiotherapy for primary retroperitoneal soft tissue sarcoma]]></article-title>
<source><![CDATA[Radiother Oncol]]></source>
<year>2002</year>
<volume>65</volume>
<numero>3</numero>
<issue>3</issue>
<page-range>137-43</page-range></nlm-citation>
</ref>
<ref id="B13">
<label>13</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Bonvalot]]></surname>
<given-names><![CDATA[S]]></given-names>
</name>
<name>
<surname><![CDATA[Gronchi]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Le Péchoux]]></surname>
<given-names><![CDATA[C]]></given-names>
</name>
<name>
<surname><![CDATA[Swallow]]></surname>
<given-names><![CDATA[CJ]]></given-names>
</name>
<name>
<surname><![CDATA[Strauss]]></surname>
<given-names><![CDATA[D]]></given-names>
</name>
<name>
<surname><![CDATA[Meeus]]></surname>
<given-names><![CDATA[P]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Preoperative radiotherapy plus surgery versus surgery alone for patients with primary retroperitoneal sarcoma (EORTC-62092: STRASS): a multicentre, open-label, randomised, phase 3 trial]]></article-title>
<source><![CDATA[Lancet Oncol]]></source>
<year>2020</year>
<volume>21</volume>
<numero>10</numero>
<issue>10</issue>
<page-range>1366-77</page-range></nlm-citation>
</ref>
<ref id="B14">
<label>14</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Gladdy]]></surname>
<given-names><![CDATA[RA]]></given-names>
</name>
<name>
<surname><![CDATA[Qin]]></surname>
<given-names><![CDATA[L-X]]></given-names>
</name>
<name>
<surname><![CDATA[Moraco]]></surname>
<given-names><![CDATA[N]]></given-names>
</name>
<name>
<surname><![CDATA[Agaram]]></surname>
<given-names><![CDATA[NP]]></given-names>
</name>
<name>
<surname><![CDATA[Brennan]]></surname>
<given-names><![CDATA[MF]]></given-names>
</name>
<name>
<surname><![CDATA[Singer]]></surname>
<given-names><![CDATA[S.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Predictors of survival and recurrence in primary leiomyosarcoma]]></article-title>
<source><![CDATA[Ann Surg Oncol.]]></source>
<year>2013</year>
<volume>20</volume>
<numero>6</numero>
<issue>6</issue>
<page-range>1851-7</page-range></nlm-citation>
</ref>
</ref-list>
</back>
</article>
