<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>1688-0420</journal-id>
<journal-title><![CDATA[Revista Uruguaya de Cardiología]]></journal-title>
<abbrev-journal-title><![CDATA[Rev.Urug.Cardiol.]]></abbrev-journal-title>
<issn>1688-0420</issn>
<publisher>
<publisher-name><![CDATA[Sociedad Uruguaya de Cardiología]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S1688-04202019000200204</article-id>
<article-id pub-id-type="doi">10.29277/cardio.34.2.16</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Nacimiento anómalo de la arteria coronaria izquierda desde la arteria pulmonar, síndrome de ALCAPA. Primer reporte de caso en Uruguay]]></article-title>
<article-title xml:lang="en"><![CDATA[Anomalous origin of the left coronary artery from the pulmonary artery, ALCAPA syndrome. First case report in Uruguay]]></article-title>
<article-title xml:lang="pt"><![CDATA[Nascimento anômalo da artéria coronária esquerda a partir da artéria pulmonar, síndrome de ALCAPA. Relato do primeiro caso no Uruguai]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Bachini]]></surname>
<given-names><![CDATA[Juan Pablo]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Amodio]]></surname>
<given-names><![CDATA[Alejandra]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Guzmán]]></surname>
<given-names><![CDATA[Rodrigo]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Fernández]]></surname>
<given-names><![CDATA[Nicolás]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Duro]]></surname>
<given-names><![CDATA[Ivanna]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Viñas]]></surname>
<given-names><![CDATA[Sergio]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Médica Uruguaya Instituto de Cardiología Integral ]]></institution>
<addr-line><![CDATA[Montevideo ]]></addr-line>
<country>Uruguay</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>08</month>
<year>2019</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>08</month>
<year>2019</year>
</pub-date>
<volume>34</volume>
<numero>2</numero>
<fpage>204</fpage>
<lpage>214</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.edu.uy/scielo.php?script=sci_arttext&amp;pid=S1688-04202019000200204&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.edu.uy/scielo.php?script=sci_abstract&amp;pid=S1688-04202019000200204&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.edu.uy/scielo.php?script=sci_pdf&amp;pid=S1688-04202019000200204&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen: El nacimiento anómalo de la arteria coronaria izquierda desde la arteria pulmonar (síndrome de ALCAPA) es una rara entidad con una mortalidad de 90% durante el primer año de vida. Este hecho hace que su presencia en el adulto sea excepcional. Presentamos el primer caso reportado en nuestro país en un adulto. Se trata de una paciente de 32 años en estudio por historia de ángor de esfuerzo en la que el ecocardiograma brindó elementos sugestivos de esta entidad que se confirmó con coronariografía. Se intervino quirúrgicamente de forma exitosa con técnica de Takeuchi.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Summary: The anomalous origin of the left coronary artery from the pulmonary artery (ALCAPA syndrome) is a rare entity with a high infant mortality rate during first year of life reaching up to 90%. This fact makes this condition extremely uncommon among adults. We report for the first time in our country an adult presentation in a 32-year-old woman. This patient presented with a history of exertional angina and a transthoracic echocardiogram showed suggestive clues for the diagnosis of ALCAPA, then confirmed with coronary angiography. The patient underwent successfull surgical correction with Takeuchi technique.]]></p></abstract>
<abstract abstract-type="short" xml:lang="pt"><p><![CDATA[Resumo: O nascimento anômalo da artéria coronária esquerda a partir da artéria pulmonar (síndrome de ALCAPA) é uma entidade rara com uma mortalidade de 90% durante o primeiro ano de vida. Este fato faz com que sua apresentação da idade adulta seja excepcional. Apresentamos o primeiro caso reportado dessa síndrome no nosso país. Se trata de uma paciente de 32 anos em estudo por uma historia de angina de esforço na qual o ecocardiograma brindou elementos sugestivos dessa entidade sendo confirmada posteriormente com angiografia coronaria. Se realizou uma intervenção cirúrgica exitosa com a técnica de Takeuchi.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Arteria pulmonar]]></kwd>
<kwd lng="es"><![CDATA[Cardiopatías congénitas]]></kwd>
<kwd lng="es"><![CDATA[Síndrome de ALCAPA]]></kwd>
<kwd lng="en"><![CDATA[Pulmonary artery]]></kwd>
<kwd lng="en"><![CDATA[Heart defects, congenital]]></kwd>
<kwd lng="en"><![CDATA[ALCAPA syndrome]]></kwd>
<kwd lng="pt"><![CDATA[Artéria pulmonar]]></kwd>
<kwd lng="pt"><![CDATA[Cardiopatias congênitas]]></kwd>
<kwd lng="pt"><![CDATA[Síndrome de ALCAPA]]></kwd>
</kwd-group>
</article-meta>
</front><back>
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