<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>1688-0390</journal-id>
<journal-title><![CDATA[Revista Médica del Uruguay]]></journal-title>
<abbrev-journal-title><![CDATA[Rev. Méd. Urug.]]></abbrev-journal-title>
<issn>1688-0390</issn>
<publisher>
<publisher-name><![CDATA[Sindicato Médico del Uruguay]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S1688-03902026000101206</article-id>
<article-id pub-id-type="doi">10.29193/rmu.42.1.12</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Características clínicas, epidemiológicas y evolutivas de los pacientes portadores de tumores del sistema nervioso central en el Hospital Pediátrico Centro Hospitalario Pereira Rossell (2017-2021)]]></article-title>
<article-title xml:lang="en"><![CDATA[Clinical, epidemiological and outcome characteristics of patients with central nervous system tumours at the Hospital Pediátrico Centro Hospitalario Pereira Rossell (2017&#8211;2021)]]></article-title>
<article-title xml:lang="pt"><![CDATA[Características clínicas, epidemiológicas e evolutivas dos pacientes portadores de tumores do sistema nervoso central no Hospital Pediátrico do Centro Hospitalar Pereira Rossell (2017&#8211;2021)]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Zunino]]></surname>
<given-names><![CDATA[Carlos]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Casuriaga]]></surname>
<given-names><![CDATA[Ana]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Morosini]]></surname>
<given-names><![CDATA[Fabiana]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Castañola]]></surname>
<given-names><![CDATA[Mariana]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Segarra]]></surname>
<given-names><![CDATA[Gabriela]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Costa]]></surname>
<given-names><![CDATA[Gonzalo]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Giachetto]]></surname>
<given-names><![CDATA[Gustavo]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Universidad de la República Facultad de Medicina Unidad Académica de Pediatría C, Hospital Pediátrico Centro Hospitalario Pereira Rossell]]></institution>
<addr-line><![CDATA[Montevideo ]]></addr-line>
<country>Uruguay</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,Universidad de la República Facultad de Medicina Unidad Académica de Neurocirugía, Hospital de Clínicas Dr. Manuel Quintela]]></institution>
<addr-line><![CDATA[Montevideo ]]></addr-line>
<country>Uruguay</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>00</month>
<year>2026</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>00</month>
<year>2026</year>
</pub-date>
<volume>42</volume>
<numero>1</numero>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.edu.uy/scielo.php?script=sci_arttext&amp;pid=S1688-03902026000101206&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.edu.uy/scielo.php?script=sci_abstract&amp;pid=S1688-03902026000101206&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.edu.uy/scielo.php?script=sci_pdf&amp;pid=S1688-03902026000101206&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen  Introducción: Los tumores primarios del sistema nervioso central (SNC) representan la segunda causa más frecuente de cáncer en la infancia. La información nacional específica sobre tumores del SNC es limitada.  Objetivo: Describir la frecuencia y las características clínicas, epidemiológicas y evolutivas de los pacientes menores de 15 años con tumores del SNC asistidos en el Servicio de Hemato-Oncología Pediátrica del Hospital Pereira Rossell durante el período 2017&#8211;2021.  Resultados: Se incluyeron 42 pacientes, el 59,5 % varones, con una mediana de edad al diagnóstico de 6 años. La localización infratentorial fue la más frecuente (52,4 %). Los síntomas predominantes fueron cefalea, vómitos e hipertensión endocraneana descompensada. El tiempo desde el inicio de síntomas al diagnóstico fue de 0&#8211;365 días (mediana de 16,5). Los astrocitomas (26,2 %) y los meduloblastomas (23,8 %) fueron los más frecuentes. El tratamiento incluyó cirugía en 85,7 %, quimioterapia en 55 % y radioterapia en 29%. La sobrevida global a tres años fue de 62,5 %, sin diferencias según localización tumoral.  Discusión: El perfil epidemiológico observado coincide con series internacionales: Este estudio aporta la primera descripción nacional y refuerza la necesidad de optimizar los tiempos diagnósticos, incorporar estudios moleculares y fortalecer el seguimiento integral, priorizando tanto la supervivencia como la calidad de vida.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Abstract  Introduction: Primary central nervous system (CNS) tumors represent the second most frequent cause of cancer in childhood. National data specifically focused on pediatric CNS tumors remain limited.  Objective: To describe the frequency and the clinical, epidemiological, and outcome characteristics of patients under 15 years of age with CNS tumors treated at the Pediatric Hemato-Oncology Service of Pereira Rossell Hospital between 2017 and 2021.  Results: A total of 42 patients were included, 59.5% male, with a median age at diagnosis of 6 years. The most common tumor location was infratentorial (52.4%). The predominant symptoms were headache, vomiting, and decompensated intracranial hypertension. The time from symptom onset to diagnosis ranged from 0 to 365 days (median 16.5). Astrocytomas (26.2%) and medulloblastomas (23.8%) were the most frequent histological types. Treatment included surgery in 85.7% of cases, chemotherapy in 55%, and radiotherapy in 29%. Overall survival at three years was 62.5%, with no significant differences according to tumor location.  Discussion: The epidemiological profile observed is consistent with international series. This study provides the first national description and highlights the need to optimize diagnostic times, incorporate molecular studies, and strengthen comprehensive follow-up, focusing not only on survival but also on quality of life.]]></p></abstract>
<abstract abstract-type="short" xml:lang="pt"><p><![CDATA[Resumo  Introdução: Os tumores primários do sistema nervoso central (SNC) representam a segunda causa mais frequente de câncer na infância. As informações nacionais específicas sobre tumores do SNC são limitadas.  Objetivo: Descrever a frequência e as características clínicas, epidemiológicas e evolutivas de pacientes menores de 15 anos com tumores do SNC atendidos no Serviço de Hemato-Oncologia Pediátrica do Hospital Pereira Rossell durante o período de 2017&#8211;2021.  Resultados: Foram incluídos 42 pacientes, sendo 59,5 % do sexo masculino, com mediana de idade ao diagnóstico de 6 anos. A localização infratentorial foi a mais frequente (52,4 %). Os sintomas predominantes foram cefaleia, vômitos e hipertensão intracraniana descompensada. O tempo desde o início dos sintomas até o diagnóstico variou de 0&#8211;365 dias (mediana de 16,5). Astrocitomas (26,2 %) e meduloblastomas (23,8 %) foram os tipos histológicos mais frequentes. O tratamento incluiu cirurgia em 85,7 %, quimioterapia em 55 % e radioterapia em 29 %. A sobrevida global em três anos foi de 62,5 %, sem diferenças segundo a localização tumoral.  Discussão: O perfil epidemiológico observado é compatível com séries internacionais. Este estudo apresenta a primeira descrição nacional e reforça a necessidade de otimizar os tempos diagnósticos, incorporar estudos moleculares e fortalecer o acompanhamento integral, priorizando tanto a sobrevida quanto a qualidade de vida.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Neoplasias encefálicas]]></kwd>
<kwd lng="es"><![CDATA[Sistema nervioso central]]></kwd>
<kwd lng="es"><![CDATA[Tumores del sistema nervioso central]]></kwd>
<kwd lng="es"><![CDATA[Pediatría]]></kwd>
<kwd lng="en"><![CDATA[Brain neoplasms]]></kwd>
<kwd lng="en"><![CDATA[Central nervous system]]></kwd>
<kwd lng="en"><![CDATA[Central nervous system tumors]]></kwd>
<kwd lng="en"><![CDATA[Pediatrics]]></kwd>
<kwd lng="pt"><![CDATA[Neoplasias encefálicas]]></kwd>
<kwd lng="pt"><![CDATA[Sistema nervoso central]]></kwd>
<kwd lng="pt"><![CDATA[Tumores do sistema nervoso central]]></kwd>
<kwd lng="pt"><![CDATA[Pediatria]]></kwd>
</kwd-group>
</article-meta>
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