<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>1688-1273</journal-id>
<journal-title><![CDATA[Anestesia Analgesia Reanimación]]></journal-title>
<abbrev-journal-title><![CDATA[Anest Analg Reanim]]></abbrev-journal-title>
<issn>1688-1273</issn>
<publisher>
<publisher-name><![CDATA[Sociedad de Anestesiología del Uruguay]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S1688-12732016000200001</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Hipertermia maligna: reporte de un caso clínico]]></article-title>
<article-title xml:lang="en"><![CDATA[Malignant hyperthermia: report of a clinical case]]></article-title>
<article-title xml:lang="pt"><![CDATA[Hipertermia maligna: relatório de um caso clínico]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Lanzilotta]]></surname>
<given-names><![CDATA[Paola]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Cristiani]]></surname>
<given-names><![CDATA[Federico]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,Universidad de la República Departamento y Cátedra de Anestesiología. Facultad de Medicina. Hospital de Clínicas Centro Hospitalario Pereira Rossell]]></institution>
<addr-line><![CDATA[ ]]></addr-line>
<country>Uruguay</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>12</month>
<year>2016</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>12</month>
<year>2016</year>
</pub-date>
<volume>29</volume>
<numero>2</numero>
<fpage>1</fpage>
<lpage>17</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.edu.uy/scielo.php?script=sci_arttext&amp;pid=S1688-12732016000200001&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.edu.uy/scielo.php?script=sci_abstract&amp;pid=S1688-12732016000200001&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.edu.uy/scielo.php?script=sci_pdf&amp;pid=S1688-12732016000200001&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen: La Hipertermia Maligna (HM), es un síndrome clínico que ocurre en pacientes susceptibles tras la exposición a un agente anestésico desencadenante. La mortalidad desciende con tratamiento específico, por lo que es fundamental su diagnóstico y tratamiento precoz. Se presenta el caso clínico de una niña de 3 años y 10 meses, en estudio por hemiparesia derecha de 3 meses de evolución. Se plantea probable enfermedad desmielinizante. Se le realizaron dos resonancias magnéticas (RNM) previas con anestesia sin incidentes. Por mala evolución de su enfermedad, se realiza nueva RNM con anestesia. A las 5 horas presenta episodio de distonías, acidosis, CPK elevada. Se interpreta como HM, se inicia tratamiento para la misma con mejoría del cuadro clínico. Presentamos este caso con el objetivo de exponer un enfoque diagnóstico y terapéutico de esta patología.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Summary: Malignant Hyperthermia (MH)is a clinical syndrome that occurs in susceptible patients after exposure to a triggering anesthetic agent. Associated mortality decreases with specific treatment, which is why its diagnosis and early treatment is essential. We present the case of a 3-year and 10-month-old girl, who presented a right hemiparesis. Possible demyelinating disease was suspected. Two previous magnetic resonance imaging (MRI) were performed under general anesthesia without complications. Due to poor evolution of his disease, new MRI is performed with anesthesia. After the procedure, she presented an episode of dystonias, acidosis, elevated CPK. It was interpreted as MH, and specific treatment was initiated instated. We present this case with the objective of exposing a diagnostic and therapeutic approach to this pathology.]]></p></abstract>
<abstract abstract-type="short" xml:lang="pt"><p><![CDATA[Resumo: A hipertermia maligna (HM), è uma sindrome clinica que ocorre em pacientes sucetíveis devido a exposição a um agente anestésico desencadeante. A mortalidade diminui com tratamento específico, para o qual é fundamental diagnostico e tratamento precoce. Apresenta-se um caso clínico de uma criança de 3 anos e 10 meses de idade, em estudo por hemiparesia direita de 3 meses de evolução. Questiona-se provável doença desmielinizante. Foram realizadas duas ressonância magnéticas (RNM) previas, sob anestesia, sem incidentes. Devido à má evolução de sua doença, realizuo-se nova RNM sob anestesia. Cinco horas após apresentou episódios de rigidez muscular, acidose e CPK elevada. Interpretou-se como HM, iniciando-se tratamento específico, obtém-se melhoria do quadro clínico. Apresentamos este caso clínico com o objetivo de expor um enfoque diagnóstico e terapêutico desta patologia.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Hipertermia maligna]]></kwd>
<kwd lng="es"><![CDATA[Dantrolene]]></kwd>
<kwd lng="es"><![CDATA[Anestesia]]></kwd>
<kwd lng="en"><![CDATA[Malignant hyperthermia]]></kwd>
<kwd lng="en"><![CDATA[Dantrolene]]></kwd>
<kwd lng="en"><![CDATA[Anesthesia]]></kwd>
<kwd lng="pt"><![CDATA[Hipertermia maligna]]></kwd>
<kwd lng="pt"><![CDATA[Dantrolene]]></kwd>
<kwd lng="pt"><![CDATA[Anestesia]]></kwd>
</kwd-group>
</article-meta>
</front><back>
<ref-list>
<ref id="B1">
<nlm-citation citation-type="journal">
<article-title xml:lang=""><![CDATA[Hipertermia Maligna]]></article-title>
<person-group person-group-type="author">
<name>
<surname><![CDATA[Escobar]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
</person-group>
<source><![CDATA[Rev Med Clin Condes]]></source>
<year>2011</year>
<volume>22</volume>
<numero>3</numero>
<issue>3</issue>
<page-range>310-5</page-range></nlm-citation>
</ref>
<ref id="B2">
<nlm-citation citation-type="journal">
<article-title xml:lang=""><![CDATA[alignant hyperthermia: a pharmacogenetic disorder]]></article-title>
<person-group person-group-type="author">
<name>
<surname><![CDATA[Stratman]]></surname>
<given-names><![CDATA[RC]]></given-names>
</name>
<name>
<surname><![CDATA[Flynn]]></surname>
<given-names><![CDATA[JD]]></given-names>
</name>
<name>
<surname><![CDATA[Hatton]]></surname>
<given-names><![CDATA[KW]]></given-names>
</name>
</person-group>
<source><![CDATA[Orthopedics]]></source>
<year>2009</year>
<volume>32</volume>
<numero>11</numero>
<issue>11</issue>
<page-range>835</page-range></nlm-citation>
</ref>
<ref id="B3">
<nlm-citation citation-type="journal">
<article-title xml:lang=""><![CDATA[Hipertermia maligna: aspectos moleculares y clínicos.]]></article-title>
<person-group person-group-type="author">
<name>
<surname><![CDATA[De Carvalho Correia]]></surname>
<given-names><![CDATA[AC]]></given-names>
</name>
<name>
<surname><![CDATA[Barros Silva]]></surname>
<given-names><![CDATA[PC]]></given-names>
</name>
<name>
<surname><![CDATA[Araújo da Silva]]></surname>
<given-names><![CDATA[B]]></given-names>
</name>
</person-group>
<source><![CDATA[Rev Bras Anestesiol]]></source>
<year>2012</year>
<volume>62</volume>
<numero>6</numero>
<issue>6</issue>
<page-range>1-10</page-range></nlm-citation>
</ref>
<ref id="B4">
<nlm-citation citation-type="journal">
<article-title xml:lang=""><![CDATA[Cardiac arrests and deaths associated with malignant hyperthermia in North America from 1987 to 2006: a report from the north american malignant hyperthermia registry of the malignant hyperthermia association of the United States.]]></article-title>
<person-group person-group-type="author">
<name>
<surname><![CDATA[Larach]]></surname>
<given-names><![CDATA[MG]]></given-names>
</name>
<name>
<surname><![CDATA[Brandom]]></surname>
<given-names><![CDATA[BW]]></given-names>
</name>
<name>
<surname><![CDATA[Allen]]></surname>
<given-names><![CDATA[GC]]></given-names>
</name>
<name>
<surname><![CDATA[Gronert]]></surname>
<given-names><![CDATA[GA]]></given-names>
</name>
<name>
<surname><![CDATA[Lehman]]></surname>
<given-names><![CDATA[EB.]]></given-names>
</name>
</person-group>
<source><![CDATA[Anesthesiology]]></source>
<year>2008</year>
<volume>108</volume>
<page-range>603-11</page-range></nlm-citation>
</ref>
<ref id="B5">
<nlm-citation citation-type="journal">
<article-title xml:lang=""><![CDATA[Trends and outcomes of malignant hyperthermia in the United States, 2000 to 2005.]]></article-title>
<person-group person-group-type="author">
<name>
<surname><![CDATA[Rosero]]></surname>
<given-names><![CDATA[EB]]></given-names>
</name>
<name>
<surname><![CDATA[Adesanya]]></surname>
<given-names><![CDATA[AO]]></given-names>
</name>
<name>
<surname><![CDATA[Timaran]]></surname>
<given-names><![CDATA[CH]]></given-names>
</name>
<name>
<surname><![CDATA[Joshi]]></surname>
<given-names><![CDATA[GP.]]></given-names>
</name>
</person-group>
<source><![CDATA[Anesthesiology]]></source>
<year>2009</year>
<volume>110</volume>
</nlm-citation>
</ref>
<ref id="B6">
<nlm-citation citation-type="journal">
<article-title xml:lang=""><![CDATA[Prevalence of malignant hyperthermia due to anesthesia in New York State, 2001-2005.]]></article-title>
<person-group person-group-type="author">
<name>
<surname><![CDATA[Brady]]></surname>
<given-names><![CDATA[JE]]></given-names>
</name>
<name>
<surname><![CDATA[Sun]]></surname>
<given-names><![CDATA[LS]]></given-names>
</name>
<name>
<surname><![CDATA[Rosenberg]]></surname>
<given-names><![CDATA[H]]></given-names>
</name>
<name>
<surname><![CDATA[Li]]></surname>
<given-names><![CDATA[G.]]></given-names>
</name>
</person-group>
<source><![CDATA[Anesth Analg]]></source>
<year>2009</year>
<volume>109</volume>
<numero>4</numero>
<issue>4</issue>
<page-range>1162-6</page-range></nlm-citation>
</ref>
<ref id="B7">
<nlm-citation citation-type="journal">
<article-title xml:lang=""><![CDATA[Malignant hyperthermia: update on susceptibility testing.]]></article-title>
<person-group person-group-type="author">
<name>
<surname><![CDATA[Litman]]></surname>
<given-names><![CDATA[RS]]></given-names>
</name>
<name>
<surname><![CDATA[Rosenberg]]></surname>
<given-names><![CDATA[H.]]></given-names>
</name>
</person-group>
<source><![CDATA[JAMA]]></source>
<year>2005</year>
<volume>293</volume>
<numero>23</numero>
<issue>23</issue>
<page-range>2918-24</page-range></nlm-citation>
</ref>
<ref id="B8">
<nlm-citation citation-type="journal">
<article-title xml:lang=""><![CDATA[Recognizing and managing a malignant hyperthermia crisis: guidelines from the European Malignant Hyperthermia Group]]></article-title>
<person-group person-group-type="author">
<name>
<surname><![CDATA[Glahn]]></surname>
<given-names><![CDATA[KP]]></given-names>
</name>
<name>
<surname><![CDATA[Ellis]]></surname>
<given-names><![CDATA[FR]]></given-names>
</name>
<name>
<surname><![CDATA[Halsall]]></surname>
<given-names><![CDATA[PJ]]></given-names>
</name>
<name>
<surname><![CDATA[Müller]]></surname>
<given-names><![CDATA[CR]]></given-names>
</name>
</person-group>
<source><![CDATA[Br J Anaesth]]></source>
<year>2010</year>
<volume>105</volume>
<numero>4</numero>
<issue>4</issue>
<page-range>417-20</page-range></nlm-citation>
</ref>
<ref id="B9">
<nlm-citation citation-type="journal">
<article-title xml:lang=""><![CDATA[Clinical presentation, treatment, and complications of malignant hyperthermia in North America from 1987 to 2006.]]></article-title>
<person-group person-group-type="author">
<name>
<surname><![CDATA[Larach]]></surname>
<given-names><![CDATA[MG]]></given-names>
</name>
<name>
<surname><![CDATA[Gronert]]></surname>
<given-names><![CDATA[GA]]></given-names>
</name>
<name>
<surname><![CDATA[Allen]]></surname>
<given-names><![CDATA[GC]]></given-names>
</name>
<name>
<surname><![CDATA[Brandom]]></surname>
<given-names><![CDATA[BW]]></given-names>
</name>
<name>
<surname><![CDATA[Lehman]]></surname>
<given-names><![CDATA[EB.]]></given-names>
</name>
</person-group>
<source><![CDATA[Anesth Analg]]></source>
<year>2010</year>
<volume>110</volume>
<numero>2</numero>
<issue>2</issue>
<page-range>498-507</page-range></nlm-citation>
</ref>
<ref id="B10">
<nlm-citation citation-type="journal">
<article-title xml:lang=""><![CDATA[Minor increase of endtidal CO2 during sevoflurane-indu ced malignant hyperthermia.]]></article-title>
<person-group person-group-type="author">
<name>
<surname><![CDATA[Bonciu]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[de la Chapelle]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Delpech]]></surname>
<given-names><![CDATA[H]]></given-names>
</name>
<name>
<surname><![CDATA[Depret]]></surname>
<given-names><![CDATA[T]]></given-names>
</name>
<name>
<surname><![CDATA[Krivosic-Horber]]></surname>
<given-names><![CDATA[R]]></given-names>
</name>
<name>
<surname><![CDATA[Aimé]]></surname>
<given-names><![CDATA[MR.]]></given-names>
</name>
</person-group>
<source><![CDATA[Paediatric Anesthesia]]></source>
<year>2007</year>
<volume>17</volume>
<numero>2</numero>
<issue>2</issue>
<page-range>180-2</page-range></nlm-citation>
</ref>
<ref id="B11">
<nlm-citation citation-type="journal">
<article-title xml:lang=""><![CDATA[Anestesia en la hipertermia maligna]]></article-title>
<person-group person-group-type="author">
<name>
<surname><![CDATA[Ortiz Gómez J]]></surname>
<given-names><![CDATA[R.]]></given-names>
</name>
</person-group>
<source><![CDATA[Rev Esp Anestesiol Reanim]]></source>
<year>2008</year>
<volume>55</volume>
<numero>3</numero>
<issue>3</issue>
<page-range>165-74</page-range></nlm-citation>
</ref>
<ref id="B12">
<nlm-citation citation-type="journal">
<article-title xml:lang=""><![CDATA[Analysis of the clinical variables associated with recrudescence after malignant hyperthermia reactions.]]></article-title>
<person-group person-group-type="author">
<name>
<surname><![CDATA[Burkman]]></surname>
<given-names><![CDATA[JM]]></given-names>
</name>
<name>
<surname><![CDATA[Posner]]></surname>
<given-names><![CDATA[KL]]></given-names>
</name>
<name>
<surname><![CDATA[Domino]]></surname>
<given-names><![CDATA[KB]]></given-names>
</name>
</person-group>
<source><![CDATA[Anesthesiology]]></source>
<year>2007</year>
<numero>5</numero>
<issue>5</issue>
<page-range>901-6</page-range></nlm-citation>
</ref>
<ref id="B13">
<nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Zhou]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
<name>
<surname><![CDATA[Allen]]></surname>
<given-names><![CDATA[PD]]></given-names>
</name>
<name>
<surname><![CDATA[Pessah]]></surname>
<given-names><![CDATA[IN]]></given-names>
</name>
<name>
<surname><![CDATA[Naguib]]></surname>
<given-names><![CDATA[M.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Trastornos neuromusculares e hipertermia maligna.]]></article-title>
<person-group person-group-type="editor">
<name>
<surname><![CDATA[Miller]]></surname>
<given-names><![CDATA[RD]]></given-names>
</name>
</person-group>
<source><![CDATA[Anestesia]]></source>
<year>2010</year>
<edition>7a ed</edition>
<page-range>947-56</page-range><publisher-loc><![CDATA[Barcelona ]]></publisher-loc>
<publisher-name><![CDATA[Elsevier]]></publisher-name>
</nlm-citation>
</ref>
<ref id="B14">
<nlm-citation citation-type="journal">
<article-title xml:lang=""><![CDATA[A clinical grading scale to predict malignant hyperthermia susceptibility]]></article-title>
<person-group person-group-type="author">
<name>
<surname><![CDATA[Larach]]></surname>
<given-names><![CDATA[MG1]]></given-names>
</name>
<name>
<surname><![CDATA[Localio]]></surname>
<given-names><![CDATA[AR]]></given-names>
</name>
<name>
<surname><![CDATA[Allen]]></surname>
<given-names><![CDATA[GC]]></given-names>
</name>
<name>
<surname><![CDATA[Denborough]]></surname>
<given-names><![CDATA[MA]]></given-names>
</name>
<name>
<surname><![CDATA[Ellis]]></surname>
<given-names><![CDATA[FR]]></given-names>
</name>
<name>
<surname><![CDATA[Gronert]]></surname>
<given-names><![CDATA[GA]]></given-names>
</name>
</person-group>
<source><![CDATA[Anesthesiology]]></source>
<year>1994</year>
<volume>80</volume>
<numero>4</numero>
<issue>4</issue>
<page-range>771-9</page-range></nlm-citation>
</ref>
<ref id="B15">
<nlm-citation citation-type="journal">
<article-title xml:lang=""><![CDATA[Síndrome de hipertermia maligna: a propósito de un caso clínico]]></article-title>
<person-group person-group-type="author">
<name>
<surname><![CDATA[Taffarel]]></surname>
<given-names><![CDATA[P]]></given-names>
</name>
<name>
<surname><![CDATA[Koffman]]></surname>
<given-names><![CDATA[F]]></given-names>
</name>
<name>
<surname><![CDATA[Zifferman]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Degiuseppe]]></surname>
<given-names><![CDATA[S]]></given-names>
</name>
<name>
<surname><![CDATA[Mansilla]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Darduin]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
</person-group>
<source><![CDATA[Arch Ar Pediatr]]></source>
<year>2015</year>
<volume>113</volume>
<numero>2</numero>
<issue>2</issue>
<page-range>e113-e6</page-range></nlm-citation>
</ref>
<ref id="B16">
<nlm-citation citation-type="journal">
<article-title xml:lang=""><![CDATA[Atypical forms of anaesthetic malignant hyperthemia.]]></article-title>
<person-group person-group-type="author">
<name>
<surname><![CDATA[Spindola]]></surname>
<given-names><![CDATA[MA]]></given-names>
</name>
</person-group>
<source><![CDATA[Rev Neuroc]]></source>
<year>2005</year>
<volume>13</volume>
<numero>3</numero>
<issue>3</issue>
</nlm-citation>
</ref>
<ref id="B17">
<nlm-citation citation-type="journal">
<article-title xml:lang=""><![CDATA[Management of malignant hyperthermia: diagnosis and treatment.]]></article-title>
<person-group person-group-type="author">
<name>
<surname><![CDATA[Schneiderbanger]]></surname>
<given-names><![CDATA[D]]></given-names>
</name>
<name>
<surname><![CDATA[Johannsen]]></surname>
<given-names><![CDATA[S]]></given-names>
</name>
<name>
<surname><![CDATA[Roewer]]></surname>
<given-names><![CDATA[N]]></given-names>
</name>
<name>
<surname><![CDATA[Schuster]]></surname>
<given-names><![CDATA[F.]]></given-names>
</name>
</person-group>
<source><![CDATA[Ther Clin Risk Manag]]></source>
<year>2014</year>
<volume>10</volume>
<page-range>355-62</page-range></nlm-citation>
</ref>
<ref id="B18">
<nlm-citation citation-type="">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Zhou]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
<name>
<surname><![CDATA[Allen]]></surname>
<given-names><![CDATA[PD]]></given-names>
</name>
<name>
<surname><![CDATA[Pessah]]></surname>
<given-names><![CDATA[IN]]></given-names>
</name>
<name>
<surname><![CDATA[Naguib]]></surname>
<given-names><![CDATA[M.]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Neuromuscular Disorders and Malignant Hyperthermia.]]></article-title>
<person-group person-group-type="editor">
<name>
<surname><![CDATA[Miller]]></surname>
<given-names><![CDATA[RD]]></given-names>
</name>
</person-group>
<source><![CDATA[Miller´s Anesthesia.]]></source>
<year></year>
<edition>7a ed</edition>
</nlm-citation>
</ref>
<ref id="B19">
<nlm-citation citation-type="journal">
<article-title xml:lang=""><![CDATA[Hipertermia maligna: ¿cómo estar preparados?]]></article-title>
<person-group person-group-type="author">
<name>
<surname><![CDATA[Corvetto]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Heider]]></surname>
<given-names><![CDATA[R]]></given-names>
</name>
<name>
<surname><![CDATA[Cavallieri]]></surname>
<given-names><![CDATA[S]]></given-names>
</name>
</person-group>
<source><![CDATA[Rev Chil Cir]]></source>
<year>2013</year>
<volume>65</volume>
</nlm-citation>
</ref>
<ref id="B20">
<nlm-citation citation-type="journal">
<article-title xml:lang=""><![CDATA[Testing for malignant hyperthermia]]></article-title>
<person-group person-group-type="author">
<name>
<surname><![CDATA[Rosenberg]]></surname>
<given-names><![CDATA[H]]></given-names>
</name>
<name>
<surname><![CDATA[Antognini]]></surname>
<given-names><![CDATA[JF]]></given-names>
</name>
<name>
<surname><![CDATA[Muldoon]]></surname>
<given-names><![CDATA[S]]></given-names>
</name>
</person-group>
<source><![CDATA[Anesthesiology]]></source>
<year>2002</year>
<volume>96</volume>
<numero>1</numero>
<issue>1</issue>
<page-range>232-7</page-range></nlm-citation>
</ref>
<ref id="B21">
<nlm-citation citation-type="book">
<source><![CDATA[MHAUS - Malignant Hyperthermia Association of the United States]]></source>
<year>2017</year>
<publisher-loc><![CDATA[USA ]]></publisher-loc>
<publisher-name><![CDATA[Asociación de Hipertermia Maligna]]></publisher-name>
</nlm-citation>
</ref>
</ref-list>
</back>
</article>
