<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>1688-1249</journal-id>
<journal-title><![CDATA[Archivos de Pediatría del Uruguay]]></journal-title>
<abbrev-journal-title><![CDATA[Arch. Pediatr. Urug.]]></abbrev-journal-title>
<issn>1688-1249</issn>
<publisher>
<publisher-name><![CDATA[Sociedad Uruguaya de Pediatría]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S1688-12492018000700382</article-id>
<article-id pub-id-type="doi">10.31134/ap.89.6.4</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Epidermólisis ampollar: a propósito de un caso clínico]]></article-title>
<article-title xml:lang="en"><![CDATA[Epydermolisis bullosa, one clinical case]]></article-title>
<article-title xml:lang="pt"><![CDATA[Epidermólise bolhosa, um caso clínico]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Vidal]]></surname>
<given-names><![CDATA[Gimena]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Carrau]]></surname>
<given-names><![CDATA[Fernanda]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Lizarraga]]></surname>
<given-names><![CDATA[Mariana]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Álvarez]]></surname>
<given-names><![CDATA[Mariela]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,UDELAR Facultad de Medicina Cátedra Dermatología]]></institution>
<addr-line><![CDATA[ ]]></addr-line>
<country>Uruguay</country>
</aff>
<aff id="Af2">
<institution><![CDATA[,UDELAR Facultad de Medicina Cátedra Dermatología]]></institution>
<addr-line><![CDATA[ ]]></addr-line>
<country>Uruguay</country>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>12</month>
<year>2018</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>12</month>
<year>2018</year>
</pub-date>
<volume>89</volume>
<numero>6</numero>
<fpage>382</fpage>
<lpage>388</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.edu.uy/scielo.php?script=sci_arttext&amp;pid=S1688-12492018000700382&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.edu.uy/scielo.php?script=sci_abstract&amp;pid=S1688-12492018000700382&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.edu.uy/scielo.php?script=sci_pdf&amp;pid=S1688-12492018000700382&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen: Las epidermólisis bullosas constituyen un grupo de genodermatosis infrecuentes caracterizadas por fragilidad cutánea y por la formación de ampollas o erosiones luego de traumas mínimos. Presentamos el caso clínico de una lactante de 15 días de vida a quien se le realizó diagnóstico de epidermólisis bullosa simple en base a la presentación clínica y a la microscopía electrónica. Con buena evolución. El interés del caso es mostrar una patología poco frecuente, destacando la importancia del correcto manejo desde el nacimiento y el abordaje multidisciplinario, ya que es una enfermedad con alto impacto en la calidad de vida.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Summary: Epidermolysis bullosa (EB) is a group of infrequent genodermatoses characterized by cutaneous fragility and blisters or erosions after minor skin trauma. This paper presents the case of a 15-day-old breastfed infant diagnosed with Epidermolysis Bullosa Simplex (EBS), it was based on clinical manifestations and electron microscopy evidence and had a subsequent favourable evolution. The case illustrates an infrequent disease and demonstrates the relevance of providing appropriate treatment immediately after childbirth, as well as the value of a multidisciplinary approach to the disease, since it has a high impact on the patients' quality of life.]]></p></abstract>
<abstract abstract-type="short" xml:lang="pt"><p><![CDATA[Resumo: Epidermólise bolhosa (EB) é um grupo de genodermatoses infrequentes caracterizadas por fragilidade cutânea e bolhas ou erosões após pequenos traumas cutâneos. Este paper apresenta o caso de uma criança amamentada com 15 dias de idade, diagnosticada com Epidermólise Bolhosa Simplex (EBS). O estudo esteve baseado em manifestações clínicas e evidências de microscopia eletrônica e teve uma evolução favorável subsequente. O caso ilustra uma doença infrequente e demonstra a importância de proporcionar tratamento adequado imediatamente após o parto, bem como o valor de uma abordagem multidisciplinar da doença, uma vez que tem alto impacto na qualidade de vida dos pacientes.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Enfermedades de la piel]]></kwd>
<kwd lng="es"><![CDATA[Epidermolisis ampollosa]]></kwd>
<kwd lng="es"><![CDATA[Terapéutica]]></kwd>
<kwd lng="es"><![CDATA[Genética]]></kwd>
<kwd lng="en"><![CDATA[Skin disease]]></kwd>
<kwd lng="en"><![CDATA[Epidermolysis bullosa]]></kwd>
<kwd lng="en"><![CDATA[Therapeutics]]></kwd>
<kwd lng="en"><![CDATA[Genetic]]></kwd>
<kwd lng="pt"><![CDATA[Dermatopatias]]></kwd>
<kwd lng="pt"><![CDATA[Epidermólise bolhosa]]></kwd>
<kwd lng="pt"><![CDATA[Terapeutica]]></kwd>
<kwd lng="pt"><![CDATA[Genética]]></kwd>
</kwd-group>
</article-meta>
</front><back>
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