<?xml version="1.0" encoding="ISO-8859-1"?><article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance">
<front>
<journal-meta>
<journal-id>1688-1249</journal-id>
<journal-title><![CDATA[Archivos de Pediatría del Uruguay]]></journal-title>
<abbrev-journal-title><![CDATA[Arch. Pediatr. Urug.]]></abbrev-journal-title>
<issn>1688-1249</issn>
<publisher>
<publisher-name><![CDATA[Sociedad Uruguaya de Pediatría]]></publisher-name>
</publisher>
</journal-meta>
<article-meta>
<article-id>S1688-12492018000200108</article-id>
<article-id pub-id-type="doi">10.31134/ap.89.2.5</article-id>
<title-group>
<article-title xml:lang="es"><![CDATA[Origen anómalo de la arteria coronaria derecha desde el tronco de la arteria pulmonar (ARCAPA)]]></article-title>
<article-title xml:lang="en"><![CDATA[Anomalous origin of the right coronary artery originating from the pulmonary trunk; ARCAPA]]></article-title>
<article-title xml:lang="pt"><![CDATA[Origem anômala da artéria coronária direita do tronco da artéria pulmonar; ARCAPA]]></article-title>
</title-group>
<contrib-group>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Franco]]></surname>
<given-names><![CDATA[Alejandro]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Cadenasso]]></surname>
<given-names><![CDATA[Betina]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Antúnez]]></surname>
<given-names><![CDATA[Serrana]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Anzíbar]]></surname>
<given-names><![CDATA[Rafael]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
<contrib contrib-type="author">
<name>
<surname><![CDATA[Touyá]]></surname>
<given-names><![CDATA[Guillermo]]></given-names>
</name>
<xref ref-type="aff" rid="Aff"/>
</contrib>
</contrib-group>
<aff id="Af1">
<institution><![CDATA[,COMEPA Unidad de Cuidados Intensivos Pediátricos y Neonatales ]]></institution>
<addr-line><![CDATA[Paysandú ]]></addr-line>
</aff>
<aff id="Af2">
<institution><![CDATA[,COMEPA  ]]></institution>
<addr-line><![CDATA[Paysandú ]]></addr-line>
</aff>
<aff id="Af3">
<institution><![CDATA[,Sanatorio Americano Centro Cardiológico ]]></institution>
<addr-line><![CDATA[ ]]></addr-line>
</aff>
<aff id="Af4">
<institution><![CDATA[,Sanatorio Americano Centro Cardiológico ]]></institution>
<addr-line><![CDATA[ ]]></addr-line>
</aff>
<pub-date pub-type="pub">
<day>00</day>
<month>04</month>
<year>2018</year>
</pub-date>
<pub-date pub-type="epub">
<day>00</day>
<month>04</month>
<year>2018</year>
</pub-date>
<volume>89</volume>
<numero>2</numero>
<fpage>108</fpage>
<lpage>112</lpage>
<copyright-statement/>
<copyright-year/>
<self-uri xlink:href="http://www.scielo.edu.uy/scielo.php?script=sci_arttext&amp;pid=S1688-12492018000200108&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.edu.uy/scielo.php?script=sci_abstract&amp;pid=S1688-12492018000200108&amp;lng=en&amp;nrm=iso"></self-uri><self-uri xlink:href="http://www.scielo.edu.uy/scielo.php?script=sci_pdf&amp;pid=S1688-12492018000200108&amp;lng=en&amp;nrm=iso"></self-uri><abstract abstract-type="short" xml:lang="es"><p><![CDATA[Resumen: Las anomalías de las arterias coronarias son una condición clínica de muy baja incidencia y de estas el origen anómalo de la arteria coronaria derecha desde el tronco de la arteria pulmonar (ARCAPA) representa cerca de 0,002% en la población general. Se puede asociar a la presencia de otras anomalías cardíacas congénitas. Presentamos el caso de una recién nacida, pretérmino de 33 semanas, gemelar, a la cual se le realiza el diagnóstico de un probable origen anómalo de coronaria derecha en un estudio ecocardiográfico de rutina realizado en la unidad de terapia intensiva. Se confirma el diagnóstico mediante cateterismo cardíaco y se realiza la corrección quirúrgica definitiva a los 6 meses de edad, estando la niña actualmente asintomática y con una calidad de vida normal. Destacamos la baja frecuencia de la ocurrencia de dicha patología, realizamos una revisión sobre los tópicos principales en el desarrollo del árbol vascular coronario y las principales anomalías del mismo. Jerarquizamos la importancia de realizar un estudio ecocardiográfico adecuado como valoración de pacientes internados en unidades de terapia intensiva neonatal.]]></p></abstract>
<abstract abstract-type="short" xml:lang="en"><p><![CDATA[Summary: Coronary artery anomalies are a clinical condition of very low incidence. Out of these, the anomalous origin of the right coronary artery from the trunk of the pulmonary artery (ARCAPA) is estimated to represent 0.002% of the general population. It may be associated with the presence of other congenital cardiac anomalies. The study presents the case of a 33 week preterm newborn twin who is diagnosed with an anomalous origin of the right coronary in a routine echocardiographic study performed in the Intensive Care Unit. The diagnosis is confirmed by cardiac catheterization and definitive surgical correction is performed at 6 months of age, the child being currently asymptomatic and enjoying a normal quality of life. We stand out the low frequency of the occurrence of this pathology. We performed a review of the main topics in the development of the coronary vascular tree and their main anomalies. We emphasize on the importance of performing an adequate Echocardiographic study as an assessment of patients admitted to Neonatal Intensive Care Units.]]></p></abstract>
<abstract abstract-type="short" xml:lang="pt"><p><![CDATA[Resumo: As anomalias das artérias coronárias representam uma condição clínica de incidência muito baixa; e a origem anômala da artéria coronária direita do tronco da artéria pulmonar (ARCAPA) representa somente uma estimativa de 0,002% na população geral. Pode estar associada à presença de outras anomalias cardíacas congênitas. Apresentamos o caso de um recém-nascido, prematuro de 33 semanas, gêmeo, diagnosticado com provável origem anômala de coronária direita em estudo ecocardiográfico de rotina realizado na Unidade de Terapia Intensiva. Confirmou-se o diagnóstico através de cateterismo cardíaco e realizou-se a correção cirúrgica definitiva aos 6 meses de idade; a doença atualmente é assintomática e a menina tem uma qualidade de vida normal. Ressaltamos a baixa frequência da ocorrência da referida patologia; realizamos uma revisão dos principais tópicos no desenvolvimento da árvore vascular coronariana e suas principais anomalias. Destacamos a importância de realizar um estudo ecocardiográfico adequado como estratégia de avaliação de pacientes internados em Unidades de Terapia Intensiva Neonatal.]]></p></abstract>
<kwd-group>
<kwd lng="es"><![CDATA[Anomalías de los vasos coronarios]]></kwd>
<kwd lng="es"><![CDATA[Anomalías de la arteria pulmonar]]></kwd>
<kwd lng="es"><![CDATA[Tronco arterial]]></kwd>
<kwd lng="en"><![CDATA[Coronary vessel anomalies]]></kwd>
<kwd lng="en"><![CDATA[Pulmonary artery abnormalities]]></kwd>
<kwd lng="en"><![CDATA[Truncus arteriosus]]></kwd>
<kwd lng="pt"><![CDATA[Anormalidades dos vasos coronários]]></kwd>
<kwd lng="pt"><![CDATA[Anormalidades da artéria pulmonar]]></kwd>
<kwd lng="pt"><![CDATA[Tronco da artéria]]></kwd>
</kwd-group>
</article-meta>
</front><back>
<ref-list>
<ref id="B1">
<label>1</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Hakim]]></surname>
<given-names><![CDATA[K]]></given-names>
</name>
<name>
<surname><![CDATA[Boussaada]]></surname>
<given-names><![CDATA[R]]></given-names>
</name>
<name>
<surname><![CDATA[Hamdi]]></surname>
<given-names><![CDATA[I]]></given-names>
</name>
<name>
<surname><![CDATA[Ouarda]]></surname>
<given-names><![CDATA[F]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Anomalous origin of the right coronary artery from the pulmonary artery]]></article-title>
<source><![CDATA[Egypt Heart J]]></source>
<year>2014</year>
<volume>66</volume>
<numero>3</numero>
<issue>3</issue>
<page-range>283-6</page-range></nlm-citation>
</ref>
<ref id="B2">
<label>2</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Lin]]></surname>
<given-names><![CDATA[S]]></given-names>
</name>
<name>
<surname><![CDATA[Wu]]></surname>
<given-names><![CDATA[S]]></given-names>
</name>
<name>
<surname><![CDATA[Lin]]></surname>
<given-names><![CDATA[H]]></given-names>
</name>
<name>
<surname><![CDATA[Chen]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Anomalous origin of the right coronary artery from the pulmonary artery in an infant]]></article-title>
<source><![CDATA[Pediatr Neonatol]]></source>
<year>2016</year>
<volume>57</volume>
<numero>5</numero>
<issue>5</issue>
<page-range>446-8</page-range></nlm-citation>
</ref>
<ref id="B3">
<label>3</label><nlm-citation citation-type="book">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Frommelt]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Frommelt]]></surname>
<given-names><![CDATA[P]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Trastornos vasculares]]></article-title>
<person-group person-group-type="editor">
<name>
<surname><![CDATA[Eidem]]></surname>
<given-names><![CDATA[B]]></given-names>
</name>
<name>
<surname><![CDATA[Cetta]]></surname>
<given-names><![CDATA[F]]></given-names>
</name>
<name>
<surname><![CDATA[O´Leary]]></surname>
<given-names><![CDATA[P.]]></given-names>
</name>
</person-group>
<source><![CDATA[Ecocardiografía en enfermedad cardíaca congénita pediátrica y de adultos]]></source>
<year>2014</year>
<page-range>342-54</page-range><publisher-name><![CDATA[Amolca]]></publisher-name>
</nlm-citation>
</ref>
<ref id="B4">
<label>4</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Montaudon]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Latrabe]]></surname>
<given-names><![CDATA[V]]></given-names>
</name>
<name>
<surname><![CDATA[Iriart]]></surname>
<given-names><![CDATA[X]]></given-names>
</name>
<name>
<surname><![CDATA[Caix]]></surname>
<given-names><![CDATA[P]]></given-names>
</name>
<name>
<surname><![CDATA[Laurent]]></surname>
<given-names><![CDATA[F]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Congenital coronary arteries anomalies review of the literature and multidetector computed tomography (MDCT)-appearance]]></article-title>
<source><![CDATA[Surg Radiol Anat]]></source>
<year>2007</year>
<volume>29</volume>
<numero>5</numero>
<issue>5</issue>
<page-range>343-55</page-range></nlm-citation>
</ref>
<ref id="B5">
<label>5</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Chaud]]></surname>
<given-names><![CDATA[G]]></given-names>
</name>
<name>
<surname><![CDATA[Parisi]]></surname>
<given-names><![CDATA[S]]></given-names>
</name>
<name>
<surname><![CDATA[Revigliono]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
<name>
<surname><![CDATA[Paladini]]></surname>
<given-names><![CDATA[G]]></given-names>
</name>
<name>
<surname><![CDATA[Rodríguez]]></surname>
<given-names><![CDATA[G]]></given-names>
</name>
<name>
<surname><![CDATA[Martínez]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Tratamiento quirúrgico de orígen anómalo de la arteria coronaria derecha con nacimiento en la arteria pulmonar]]></article-title>
<source><![CDATA[Cir Cardiov]]></source>
<year>2016</year>
<volume>23</volume>
<numero>3</numero>
<issue>3</issue>
<page-range>136-7</page-range></nlm-citation>
</ref>
<ref id="B6">
<label>6</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Al-Dairy]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Rezaei]]></surname>
<given-names><![CDATA[Y]]></given-names>
</name>
<name>
<surname><![CDATA[Pouraliakbar]]></surname>
<given-names><![CDATA[H]]></given-names>
</name>
<name>
<surname><![CDATA[Mahdavi]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Bayati]]></surname>
<given-names><![CDATA[P]]></given-names>
</name>
<name>
<surname><![CDATA[Gholampour]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Surgical repair for anomalous origin of the right coronary artery from the pulmonary artery]]></article-title>
<source><![CDATA[Korean Circ J]]></source>
<year>2017</year>
<volume>47</volume>
<numero>1</numero>
<issue>1</issue>
<page-range>144-7</page-range></nlm-citation>
</ref>
<ref id="B7">
<label>7</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Mahdavi]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Vahidshahi]]></surname>
<given-names><![CDATA[K]]></given-names>
</name>
<name>
<surname><![CDATA[Tehrani]]></surname>
<given-names><![CDATA[R]]></given-names>
</name>
<name>
<surname><![CDATA[Ali-Akbar]]></surname>
<given-names><![CDATA[H]]></given-names>
</name>
<name>
<surname><![CDATA[Godarzi]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Anomalous right coronary artery from the pulmonary artery (ARCAPA), and aberrant right subclavian artery in a 2-month infant with heart failure]]></article-title>
<source><![CDATA[Cardiol Young]]></source>
<year>2014</year>
<volume>24</volume>
<numero>5</numero>
<issue>5</issue>
<page-range>935-7</page-range></nlm-citation>
</ref>
<ref id="B8">
<label>8</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Lluri]]></surname>
<given-names><![CDATA[G]]></given-names>
</name>
<name>
<surname><![CDATA[Aboulhosn]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Coronary arterial development a review of normal and congenitally anomalous patterns]]></article-title>
<source><![CDATA[Clin Cardiol]]></source>
<year>2014</year>
<volume>37</volume>
<numero>2</numero>
<issue>2</issue>
<page-range>126-30</page-range></nlm-citation>
</ref>
<ref id="B9">
<label>9</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Hauser]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Congenital anomalies of the coronary arteries]]></article-title>
<source><![CDATA[Heart]]></source>
<year>2005</year>
<volume>91</volume>
<numero>9</numero>
<issue>9</issue>
<page-range>1240-5</page-range></nlm-citation>
</ref>
<ref id="B10">
<label>10</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Kochar]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Kiefer]]></surname>
<given-names><![CDATA[T]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Coronary Artery Anomalies When You Need to Worry]]></article-title>
<source><![CDATA[Curr Cardiol Rep]]></source>
<year>2017</year>
<volume>19</volume>
<numero>5</numero>
<issue>5</issue>
<page-range>39</page-range></nlm-citation>
</ref>
<ref id="B11">
<label>11</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Kim]]></surname>
<given-names><![CDATA[K]]></given-names>
</name>
<name>
<surname><![CDATA[Jo]]></surname>
<given-names><![CDATA[E]]></given-names>
</name>
<name>
<surname><![CDATA[Yu]]></surname>
<given-names><![CDATA[J]]></given-names>
</name>
<name>
<surname><![CDATA[Kil]]></surname>
<given-names><![CDATA[H]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Anomalous right coronary artery from pulmonary artery discovered incidentally in an asymptomatic young infant]]></article-title>
<source><![CDATA[Korean J Pediatr]]></source>
<year>2016</year>
<volume>59</volume>
<numero>^s1</numero>
<issue>^s1</issue>
<supplement>1</supplement>
<page-range>S80-3</page-range></nlm-citation>
</ref>
<ref id="B12">
<label>12</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Balakrishna]]></surname>
<given-names><![CDATA[P]]></given-names>
</name>
<name>
<surname><![CDATA[Illovsky]]></surname>
<given-names><![CDATA[M]]></given-names>
</name>
<name>
<surname><![CDATA[Al-Saghir]]></surname>
<given-names><![CDATA[Y]]></given-names>
</name>
<name>
<surname><![CDATA[Minhas]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Anomalous origin of right coronary artery originating from the pulmonary trunk (ARCAPA) an incidental finding in a patient presenting whit chest pain. Open access case report]]></article-title>
<source><![CDATA[Cureus]]></source>
<year>2017</year>
<volume>9</volume>
<numero>4</numero>
<issue>4</issue>
</nlm-citation>
</ref>
<ref id="B13">
<label>13</label><nlm-citation citation-type="journal">
<person-group person-group-type="author">
<name>
<surname><![CDATA[Mittal]]></surname>
<given-names><![CDATA[K]]></given-names>
</name>
<name>
<surname><![CDATA[Dey]]></surname>
<given-names><![CDATA[A]]></given-names>
</name>
<name>
<surname><![CDATA[Gadewar]]></surname>
<given-names><![CDATA[R]]></given-names>
</name>
<name>
<surname><![CDATA[Sharma]]></surname>
<given-names><![CDATA[R]]></given-names>
</name>
<name>
<surname><![CDATA[Pandit]]></surname>
<given-names><![CDATA[N]]></given-names>
</name>
<name>
<surname><![CDATA[Rajput]]></surname>
<given-names><![CDATA[P]]></given-names>
</name>
</person-group>
<article-title xml:lang=""><![CDATA[Rare case of truncus arteriosus with anomalous origin of the right coronary artery from the pulmonary artery (ARCAPA) and unilateral left pulmonary artery agenesis]]></article-title>
<source><![CDATA[Jpn J Radiol]]></source>
<year>2015</year>
<volume>33</volume>
<numero>4</numero>
<issue>4</issue>
<page-range>220-4</page-range></nlm-citation>
</ref>
</ref-list>
</back>
</article>
