Resumo

PEREIRA, Laura et al. Hemophagocytic lymphohistiocytosis. Report of a clinical case. Arch. Pediatr. Urug. [online]. 2018, vol.89, n.2, pp.122-128. ISSN 0004-0584.  https://doi.org/10.31134/ap.89.2.7.

Hemophagocytic lymphohistiocytosis includes an heterogeneous group of diseases that can occur at any age. The genetic or primary form manifests before the first year of life and the acquired or secondary form is usually related to infectious, oncological, rheumatic or immunologic processes and can be seen at any age. This diagnosis requires high rate of suspicion and it is confirmed by the Histiocyte Society’s criteria. Death rate related to this condition is extremely high.This case report aims to raise awareness among pediatricians with the intention of obtaining an early diagnosis that allows clinicians to initiate effective and directed treatment opportunely.

Palavras-chave : Hemophagocytic lymphohistiocytosis.

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