Servicios Personalizados
Revista
Articulo
Links relacionados
Compartir
Archivos de Pediatría del Uruguay
versión On-line ISSN 1688-1249
Resumen
DEUTSCH, Ilse y PINCHAK, María Catalina. Microlitiasis alveolar pulmonar: A propósito de un caso . Arch. Pediatr. Urug. [online]. 2012, vol.83, n.4, pp.256-261. ISSN 1688-1249.
Summary Pulmonary alveolar microlithiasis is a rare disease characterized by intra-alveolar deposit of calcium and phosphate concretions. Presentation in children is very unusual given its chronic progression over several years, with marked clinical-radiological dissociation. In its pathogenesis is involved a gene, recently described, encoding a sodium phosphate co-transporter expressed in lung tissue. Usually evolves from an asymptomatic stage of variable duration, adding coughing and difficulty breathing, determining respiratory failure and cor pulmonale in advanced stages. A pediatric case illustrating clinical features and difficulties in diagnosis is reported.
Palabras clave : LUNG DISEASES, INTERSTITIAL; LITHIASIS; CALCIUM PHOSPHATES.