Abstract

GONZALEZ, Gabriel; PEREZ, Rosana; SATRIANO, Rosario  and  ROTONDO, Ma. Teresa. Neuro-Behçet: a propósito de un caso clínico. Arch. Pediatr. Urug. [online]. 2007, vol.78, n.2, pp.139-145. ISSN 1688-1249.

Summary The case of a 7-year- old Uruguayan boy with recurrent episodes of fever, oral aphthas lesions and meningoencephalitis with elevated protein levels and lymphocytic pleocytosis is presented. Other diagnoses were excluded. MRI showed in acute stages CNS involvement in iso- or hipointense in T1- weighted images and hyperintense in T2-weighted or fluid- attenuated inversion recovery (FLAIR) images in mesodiencephalic junction, cerebellar peduncles, pons, corpus callosum, basal ganglia and internal capsule, and cerebral hemispheres. In the evolution skin lesions appeared, fulfilling the International Study Group Criteria for the Diagnosis of Behçet' Disease. Corticosteroids and immunosuppressant treatment was done. The main difficulty in children is having all the criteria for diagnosis; especially when recurrent genital ulceration and eye lesion rarely appear at this age

Keywords : BEHÇET SYNDROME-diagnosis; BEHÇET SYNDROME-therapy; VASCULITIS; DIAGNOSIS, DIFFERENTIAL.

        · abstract in Spanish     · text in Spanish     · Spanish ( pdf )