Abstract

BACHINI, Juan Pablo et al. Anomalous origin of the left coronary artery from the pulmonary artery, ALCAPA syndrome. First case report in Uruguay. Rev.Urug.Cardiol. [online]. 2019, vol.34, n.2, pp.204-214.  Epub Aug 01, 2019. ISSN 0797-0048.  https://doi.org/10.29277/cardio.34.2.16.

The anomalous origin of the left coronary artery from the pulmonary artery (ALCAPA syndrome) is a rare entity with a high infant mortality rate during first year of life reaching up to 90%. This fact makes this condition extremely uncommon among adults. We report for the first time in our country an adult presentation in a 32-year-old woman. This patient presented with a history of exertional angina and a transthoracic echocardiogram showed suggestive clues for the diagnosis of ALCAPA, then confirmed with coronary angiography. The patient underwent successfull surgical correction with Takeuchi technique.

Keywords : Pulmonary artery; Heart defects, congenital; ALCAPA syndrome.

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