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Archivos de Pediatría del Uruguay

versión impresa ISSN 0004-0584


CAPOTE, Gabriela; CERISOLA, Alfredo  y  SCAVONE, Cristina. Espasmos epilépticos de inicio tardío: presentación de un caso clínico. Arch. Pediatr. Urug. [online]. 2009, vol.80, n.2, pp. 118-122. ISSN 0004-0584.

Introduction: epileptic spasms is a specific type of epileptic crisis characterized by a brief muscular contraction of extremities and upper body. The presentation during the first year of age is in bursts of contractions and an electroencephalogram pattern of West Syndrome disease. The classification of these spasms after the first year of age with a varied electroencephalogram pattern is interesting. Clincal case: a three year old girl with no personal history starts with epileptic spasms and a deficiency of acquired conducts. Misleading sight, reaction loss and drooling and chewing automatisms appeared in the evolution. The electroencephalogram showed a slower rhythm with paroxistic bilateral frontal–temporal activity with no clear lateralization signs. The image and metabolic studies were normal. Antiepileptic drugs controlled the crisis and there was a normalization of the electroencephalogram pattern at the beginning which was altered again in the evolution as well as the conducts. Discussion: clinical and electroencephalogram findings such as the ones in this patient support the diagnosis of a non described previous epileptic encephalopathy cataloged between West Syndrome and Lennox–Gastaut Syndrome.


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